Fatal Familial Insomnia
• Fatal familial insomnia is a very rare genetic brain disorder in which there is a degeneration of anterior and dorsomedial nuclei of the thalamus.
• Insomnia is a prominent early symptom.
Patients with Fatal familial insomnia develop progressive autonomic dysfunction, followed by difficulty speaking, coma, and death.

• Fatal familial insomnia is believed to be caused by a mutation in the prion gene similar to Mad Cow Disease
Posted on June 13, 2010
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